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KMID : 1034720190110010091
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Journal of Neurosonology and Neuroimaging
2019 Volume.11 No. 1 p.91 ~ p.95
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Gorham-Stout Disease of the Cranial Bone Causing Recurrent Cerebrospinal Fluid Rhinorrhea and Bacterial Meningitis
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Kim Jin-Ah
Son Hyo-Shin
Yoon Sung-Joon
Kwon Hyung-Min
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Abstract
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Gorham-Stout disease (GSD) is a rare disorder characterized by the proliferation of vascular tissue in the bones and the progressive destruction of bones. We report the case of a 25-year-old man with GSD involving the cranial bone, who presented with recurrent cerebrospinal fluid (CSF) rhinorrhea and bacterial meningitis. Because of the rarity of this disease, arriving at the diagnosis of GSD was challenging. After excluding other etiologies, the clinical and radiological findings helped us to make a diagnosis of GSD. Serial computerized tomography scans and brain magnetic resonance imaging findings over a long period of time were crucial in the diagnosis of GSD. The patient required surgical repair of the CSF leak using a septal flap. Recently, the efficacy of sirolimus has been shown in several studies. Therefore, our patient was referred to a specialist in this disease, and sirolimus was started.
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KEYWORD
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Gorham-Stout disease, Cerebrospinal f luid rhinorrhea, Bacterial meningitis
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